članak: 1 od 1  
Vojnosanitetski pregled
2011, vol. 68, br. 3, str. 270-273
jezik rada: srpski
prikaz slučaja
doi:10.2298/VSP1103270P

Kongenitalne intestinalne limfangiektazije
aUniverzitet u Beogradu, Medicinski fakultet, Klinički centar Srbije
bKlinički centar Srbije, Institut za endokrinologiju, dijabetes i bolesti metabolizma, Beograd

e-adresa: dr.popovic@sezampro.rs

Sažetak

Uvod. Kongenitalne crevne limfangiektazije su oboljenje iz grupe enteropatija sa gubitkom proteina. Karakterišu se proširenjem limfnih sudova u zidu i mezenterijumu tankog creva. Klinički se manifestuju malapsorpcijom, malnutricijom, steatorejom, edemima i izlivima. Terapija uključuje dijetu i primenu lekova. Prikaz bolesnika. Muškarac, star 19 godina, primljen je zbog oticanja trbuha, proliva, malaksalosti i zamaranja. Fizikalni pregled ukazao je na zastoj u rastu i razvoju, ascites i limfedem leve podlaktice i šake. Laboratorijske analize pokazale su hiposideremijsku anemiju, limfopeniju, malapsorpciju, pozitivan zapaljenski sindrom i urinarnu infekciju. Dijagnostičkim procedurama dokazano je prisustvo limfangiektazija u celom tankom crevu. Bolesnik je lečen dijetom, somatotropinom i suportivnom terapijom. Primenjena terapija dovela je do značajnog kliničkog i laboratorijskog poboljšanja. Zaključak. Kongenitalne limfangiektazije su retko oboljenje koje se, uglavnom, dijagnostikuju u dečijem uzrastu. One mogu biti uzrok brojnih komplikacija koje se sprečavaju ranom dijagnostikom i primenom adekvatnog lečenja.

Ključne reči

crevo, tanko, bolesti; limfangiektazija, intestinalna; anomalije; dijagnoza, diferencijalna; lečenje lekovima

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